TTN c.533C>A ;(p.A178D)

Variant ID: 2-179665172-G-T

NM_001267550.1(TTN):c.533C>A;(p.A178D)

This variant was identified in 11 publications

View GRCh38 version.




Publications:


Beyond gene-disease validity: capturing structured data on inheritance, allelic-requirement, disease-relevant variant classes, and disease mechanism for inherited cardiac conditions.

Medrxiv : The Preprint Server For Health Sciences
Josephs, Katherine S KS; Roberts, Angharad M AM; Theotokis, Pantazis P; Walsh, Roddy R; Ostrowski, Philip J PJ; Edwards, Matthew M; Fleming, Andrew A; Thaxton, Courtney C; Roberts, Jason D JD; Care, Melanie M; Zareba, Wojciech W; Adler, Arnon A; Sturm, Amy C AC; Tadros, Rafik R; Novelli, Valeria V; Owens, Emma E; Bronicki, Lucas L; Jarinova, Olga O; Callewaert, Bert B; Peters, Stacey S; Lumbers, Tom T; Jordan, Elizabeth E; Asatryan, Babken B; Krishnan, Neesha N; Hershberger, Ray E RE; Chahal, C Anwar A CAA; Landstrom, Andrew P AP; James, Cynthia C; McNally, Elizabeth M EM; Judge, Daniel P DP; van Tintelen, Peter P; Wilde, Arthur A; Gollob, Michael M; Ingles, Jodie J; Ware, James S JS
Publication Date: 2023-04-03

Variant appearance in text: TTN: Ala178Asp
PubMed Link: 37066275
Variant Present in the following documents:
  • media-2.xlsx, sheet 2
View BVdb publication page



Structural and signaling proteins in the Z-disk and their role in cardiomyopathies.

Frontiers In Physiology
Noureddine, Maya M; Gehmlich, Katja K
Publication Date: 2023

Variant appearance in text: TTN: Ala178Asp
PubMed Link: 36935760
Variant Present in the following documents:
  • Main text
  • fphys-14-1143858.pdf
View BVdb publication page



Protein Quality Control at the Sarcomere: Titin Protection and Turnover and Implications for Disease Development.

Frontiers In Physiology
Kötter, Sebastian S; Krüger, Martina M
Publication Date: 2022

Variant appearance in text: TTN: A178D
PubMed Link: 35846001
Variant Present in the following documents:
  • Main text
  • fphys-13-914296.pdf
View BVdb publication page



Overlap phenotypes of the left ventricular noncompaction and hypertrophic cardiomyopathy with complex arrhythmias and heart failure induced by the novel truncated DSC2 mutation.

Orphanet Journal Of Rare Diseases
Lin, Yubi Y; Huang, Jiana J; Zhu, Zhiling Z; Zhang, Zuoquan Z; Xian, Jianzhong J; Yang, Zhe Z; Qin, Tingfeng T; Chen, Linxi L; Huang, Jingmin J; Huang, Yin Y; Wu, Qiaoyun Q; Hu, Zhenyu Z; Lin, Xiufang X; Xu, Geyang G
Publication Date: 2021-11-24

Variant appearance in text: TTN: 533C>A; A178D
PubMed Link: 34819141
Variant Present in the following documents:
  • Main text
View BVdb publication page



Overlap phenotypes of the left ventricular noncompaction and hypertrophic cardiomyopathy with complex arrhythmias and heart failure induced by the novel truncated DSC2 mutation.

Orphanet Journal Of Rare Diseases
Lin, Yubi Y; Huang, Jiana J; Zhu, Zhiling Z; Zhang, Zuoquan Z; Xian, Jianzhong J; Yang, Zhe Z; Qin, Tingfeng T; Chen, Linxi L; Huang, Jingmin J; Huang, Yin Y; Wu, Qiaoyun Q; Hu, Zhenyu Z; Lin, Xiufang X; Xu, Geyang G
Publication Date: 2021-11-24

Variant appearance in text: TTN: 533C>A; A178D
PubMed Link: 34819141
Variant Present in the following documents:
  • Main text
View BVdb publication page



Functional analysis of a gene-edited mouse model to gain insights into the disease mechanisms of a titin missense variant.

Basic Research In Cardiology
Jiang, He H; Hooper, Charlotte C; Kelly, Matthew M; Steeples, Violetta V; Simon, Jillian N JN; Beglov, Julia J; Azad, Amar J AJ; Leinhos, Lisa L; Bennett, Pauline P; Ehler, Elisabeth E; Kalisch-Smith, Jacinta I JI; Sparrow, Duncan B DB; Fischer, Roman R; Heilig, Raphael R; Isackson, Henrik H; Ehsan, Mehroz M; Patone, Giannino G; Huebner, Norbert N; Davies, Benjamin B; Watkins, Hugh H; Gehmlich, Katja K
Publication Date: 2021-02-26

Variant appearance in text: TTN: A178D
PubMed Link: 33637999
Variant Present in the following documents:
  • Main text
  • 395_2021_Article_853.pdf
View BVdb publication page



Functional analysis of a gene-edited mouse model to gain insights into the disease mechanisms of a titin missense variant.

Basic Research In Cardiology
Jiang, He H; Hooper, Charlotte C; Kelly, Matthew M; Steeples, Violetta V; Simon, Jillian N JN; Beglov, Julia J; Azad, Amar J AJ; Leinhos, Lisa L; Bennett, Pauline P; Ehler, Elisabeth E; Kalisch-Smith, Jacinta I JI; Sparrow, Duncan B DB; Fischer, Roman R; Heilig, Raphael R; Isackson, Henrik H; Ehsan, Mehroz M; Patone, Giannino G; Huebner, Norbert N; Davies, Benjamin B; Watkins, Hugh H; Gehmlich, Katja K
Publication Date: 2021-02-26

Variant appearance in text: TTN: A178D
PubMed Link: 33637999
Variant Present in the following documents:
  • Main text
  • 395_2021_Article_853.pdf
View BVdb publication page



Making sense of missense variants in TTN-related congenital myopathies.

Acta Neuropathologica
Rees, Martin M; Nikoopour, Roksana R; Fukuzawa, Atsushi A; Kho, Ay Lin AL; Fernandez-Garcia, Miguel A MA; Wraige, Elizabeth E; Bodi, Istvan I; Deshpande, Charu C; Özdemir, Özkan Ö; Daimagüler, Hülya-Sevcan HS; Pfuhl, Mark M; Holt, Mark M; Brandmeier, Birgit B; Grover, Sarah S; Fluss, Joël J; Longman, Cheryl C; Farrugia, Maria Elena ME; Matthews, Emma E; Hanna, Michael M; Muntoni, Francesco F; Sarkozy, Anna A; Phadke, Rahul R; Quinlivan, Ros R; Oates, Emily C EC; Schröder, Rolf R; Thiel, Christian C; Reimann, Jens J; Voermans, Nicol N; Erasmus, Corrie C; Kamsteeg, Erik-Jan EJ; Konersman, Chaminda C; Grosmann, Carla C; McKee, Shane S; Tirupathi, Sandya S; Moore, Steven A SA; Wilichowski, Ekkehard E; Hobbiebrunken, Elke E; Dekomien, Gabriele G; Richard, Isabelle I; Van den Bergh, Peter P; Domínguez-González, Cristina C; Cirak, Sebahattin S; Ferreiro, Ana A; Jungbluth, Heinz H; Gautel, Mathias M
Publication Date: 2021-03

Variant appearance in text: TTN: Ala178Asp
PubMed Link: 33449170
Variant Present in the following documents:
  • Main text
  • 401_2020_Article_2257.pdf
View BVdb publication page



Is Gene-Size an Issue for the Diagnosis of Skeletal Muscle Disorders?

Journal Of Neuromuscular Diseases
Savarese, Marco M; Välipakka, Salla S; Johari, Mridul M; Hackman, Peter P; Udd, Bjarne B
Publication Date: 2020

Variant appearance in text: TTN: Ala178Asp
PubMed Link: 32176652
Variant Present in the following documents:
  • Main text
  • jnd-7-jnd190459.pdf
View BVdb publication page



Systematic Review of Genotype-Phenotype Correlations in Noncompaction Cardiomyopathy.

Journal Of The American Heart Association
van Waning, Jaap I JI; Moesker, Joost J; Heijsman, Daphne D; Boersma, Eric E; Majoor-Krakauer, Danielle D
Publication Date: 2019-12-03

Variant appearance in text: TTN: 533C>A; Ala178Asp
PubMed Link: 31771441
Variant Present in the following documents:
  • JAH3-8-e012993-s001.pdf
  • JAH3-8-e012993.pdf
View BVdb publication page



Non-sarcomeric causes of heart failure.

Biophysical Reviews
Gehmlich, Katja K; Ehler, Elisabeth E
Publication Date: 2018-08

Variant appearance in text: TTN: A178D
PubMed Link: 30008146
Variant Present in the following documents:
  • Main text
View BVdb publication page



When signalling goes wrong: pathogenic variants in structural and signalling proteins causing cardiomyopathies.

Journal Of Muscle Research And Cell Motility
Ehsan, Mehroz M; Jiang, He H; L Thomson, Kate K; Gehmlich, Katja K
Publication Date: 2017-08

Variant appearance in text: TTN: A178D
PubMed Link: 29119312
Variant Present in the following documents:
  • Main text
  • 10974_2017_Article_9487.pdf
View BVdb publication page



Combination of Whole Genome Sequencing, Linkage, and Functional Studies Implicates a Missense Mutation in Titin as a Cause of Autosomal Dominant Cardiomyopathy With Features of Left Ventricular Noncompaction.

Circulation. Cardiovascular Genetics
Hastings, Robert R; de Villiers, Carin P CP; Hooper, Charlotte C; Ormondroyd, Liz L; Pagnamenta, Alistair A; Lise, Stefano S; Salatino, Silvia S; Knight, Samantha J L SJ; Taylor, Jenny C JC; Thomson, Kate L KL; Arnold, Linda L; Chatziefthimiou, Spyros D SD; Konarev, Petr V PV; Wilmanns, Matthias M; Ehler, Elisabeth E; Ghisleni, Andrea A; Gautel, Mathias M; Blair, Edward E; Watkins, Hugh H; Gehmlich, Katja K
Publication Date: 2016-10

Variant appearance in text: TTN: 533C>A; A178D
PubMed Link: 27625337
Variant Present in the following documents:
  • Main text
  • hcg-9-426-s002.pdf
  • hcg-9-426-s001.pdf
  • hcg-9-426.pdf
View BVdb publication page