Publications:

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Neurodegenerative Diseases: From Dysproteostasis, Altered Calcium Signalosome to Selective Neuronal Vulnerability to AAV-Mediated Gene Therapy.

International Journal Of Molecular Sciences

Quach, Tam T TT; Stratton, Harrison J HJ; Khanna, Rajesh R; Mackey-Alfonso, Sabrina S; Deems, Nicolas N; Honnorat, Jérome J; Meyer, Kathrin K; Duchemin, Anne-Marie AM

Publication Date: 2022-11-16

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PubMed Link: 36430666

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Translational potential of base-editing tools for gene therapy of monogenic diseases.

Frontiers In Bioengineering And Biotechnology

Reshetnikov, Vasiliy V VV; Chirinskaite, Angelina V AV; Sopova, Julia V JV; Ivanov, Roman A RA; Leonova, Elena I EI

Publication Date: 2022

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PubMed Link: 36032737

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Applications of Various Types of Nanomaterials for the Treatment of Neurological Disorders.

Nanomaterials (Basel, Switzerland)

Waris, Abdul A; Ali, Asmat A; Khan, Atta Ullah AU; Asim, Muhammad M; Zamel, Doaa D; Fatima, Kinza K; Raziq, Abdur A; Khan, Muhammad Ajmal MA; Akbar, Nazia N; Baset, Abdul A; Abourehab, Mohammed A S MAS

Publication Date: 2022-06-22

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PubMed Link: 35807977

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• nanomaterials-12-02140.pdf

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Copper, Iron, and Manganese Toxicity in Neuropsychiatric Conditions.

International Journal Of Molecular Sciences

Tarnacka, Beata B; Jopowicz, Anna A; Maślińska, Maria M

Publication Date: 2021-07-22

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PubMed Link: 34360586

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• ijms-22-07820.pdf

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Caenorhabditis elegans as a model system for studying aging-associated neurodegenerative diseases.

Translational Medicine Of Aging

Van Pelt, Kate M KM; Truttmann, Matthias C MC

Publication Date: 2020

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PubMed Link: 34327290

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Utilising Induced Pluripotent Stem Cells in Neurodegenerative Disease Research: Focus on Glia.

International Journal Of Molecular Sciences

Albert, Katrina K; Niskanen, Jonna J; Kälvälä, Sara S; Lehtonen, Šárka Š

Publication Date: 2021-04-21

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PubMed Link: 33919317

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Characterization of brain-derived extracellular vesicles reveals changes in cellular origin after stroke and enrichment of the prion protein with a potential role in cellular uptake.

Journal Of Extracellular Vesicles

Brenna, Santra S; Altmeppen, Hermann C HC; Mohammadi, Behnam B; Rissiek, Björn B; Schlink, Florence F; Ludewig, Peter P; Krisp, Christoph C; Schlüter, Hartmut H; Failla, Antonio Virgilio AV; Schneider, Carola C; Glatzel, Markus M; Puig, Berta B; Magnus, Tim T

Publication Date: 2020-08-27

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PubMed Link: 32944194

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• ZJEV_9_1809065.pdf

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The PERK-Dependent Molecular Mechanisms as a Novel Therapeutic Target for Neurodegenerative Diseases.

International Journal Of Molecular Sciences

Rozpędek-Kamińska, Wioletta W; Siwecka, Natalia N; Wawrzynkiewicz, Adam A; Wojtczak, Radosław R; Pytel, Dariusz D; Diehl, J Alan JA; Majsterek, Ireneusz I

Publication Date: 2020-03-19

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PubMed Link: 32204380

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• ijms-21-02108.pdf

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The basis of clinicopathological heterogeneity in TDP-43 proteinopathy.

Acta Neuropathologica

Kawakami, Ito I; Arai, Tetsuaki T; Hasegawa, Masato M

Publication Date: 2019-11

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PubMed Link: 31555895

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• 401_2019_Article_2077.pdf

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Small Molecules Attenuate the Interplay between Conformational Fluctuations, Early Oligomerization and Amyloidosis of Alpha Synuclein.

Scientific Reports

Ghosh, Sumanta S; Kundu, Amrita A; Chattopadhyay, Krishnananda K

Publication Date: 2018-04-03

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PubMed Link: 29615762

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• 41598_2018_Article_23718.pdf

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Inhibition of group-I metabotropic glutamate receptors protects against prion toxicity.

Plos Pathogens

Goniotaki, Despoina D; Lakkaraju, Asvin K K AKK; Shrivastava, Amulya N AN; Bakirci, Pamela P; Sorce, Silvia S; Senatore, Assunta A; Marpakwar, Rajlakshmi R; Hornemann, Simone S; Gasparini, Fabrizio F; Triller, Antoine A; Aguzzi, Adriano A

Publication Date: 2017-11

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PubMed Link: 29176838

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• ppat.1006733.pdf

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The relevance of contact-independent cell-to-cell transfer of TDP-43 and SOD1 in amyotrophic lateral sclerosis.

Biochimica Et Biophysica Acta. Molecular Basis Of Disease

Hanspal, Maya A MA; Dobson, Christopher M CM; Yerbury, Justin J JJ; Kumita, Janet R JR

Publication Date: 2017-11

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PubMed Link: 28711596

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Emerging roles of extracellular vesicles in neurodegenerative disorders: focus on HIV-associated neurological complications.

Cell Death & Disease

Hu, Guoku G; Yang, Lu L; Cai, Yu Y; Niu, Fang F; Mezzacappa, Frank F; Callen, Shannon S; Fox, Howard S HS; Buch, Shilpa S

Publication Date: 2016-11-24

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PubMed Link: 27882942

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The unfolded protein response: mechanisms and therapy of neurodegeneration.

Brain : A Journal Of Neurology

Smith, Heather L HL; Mallucci, Giovanna R GR

Publication Date: 2016-08

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PubMed Link: 27190028

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• aww101.pdf

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The Unfolded Protein Response and the Role of Protein Disulfide Isomerase in Neurodegeneration.

Frontiers In Cell And Developmental Biology

Perri, Emma R ER; Thomas, Colleen J CJ; Parakh, Sonam S; Spencer, Damian M DM; Atkin, Julie D JD

Publication Date: 2015

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PubMed Link: 26779479

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Using C. elegans to discover therapeutic compounds for ageing-associated neurodegenerative diseases.

Chemistry Central Journal

Chen, Xi X; Barclay, Jeff W JW; Burgoyne, Robert D RD; Morgan, Alan A

Publication Date: 2015

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PubMed Link: 26617668

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Degradation of misfolded proteins in neurodegenerative diseases: therapeutic targets and strategies.

Experimental & Molecular Medicine

Ciechanover, Aaron A; Kwon, Yong Tae YT

Publication Date: 2015-03-13

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PubMed Link: 25766616

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Evidence for prion-like mechanisms in several neurodegenerative diseases: potential implications for immunotherapy.

Clinical & Developmental Immunology

Marciniuk, Kristen K; Taschuk, Ryan R; Napper, Scott S

Publication Date: 2013

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PubMed Link: 24228054

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• CDI2013-473706.pdf

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Disulfide bonding in neurodegenerative misfolding diseases.

International Journal Of Cell Biology

Mossuto, Maria Francesca MF

Publication Date: 2013

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PubMed Link: 23983694

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Redox processes in neurodegenerative disease involving reactive oxygen species.

Current Neuropharmacology

Kovacic, Peter P; Somanathan, Ratnasamy R

Publication Date: 2012-12

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PubMed Link: 23730253

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• CN-10-289.pdf

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Amyotrophic lateral sclerosis and organ donation: is there risk of disease transmission?

Annals Of Neurology

Holmes, Brandon B BB; Diamond, Marc I MI

Publication Date: 2012-12

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PubMed Link: 23280834

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Weighted gene co-expression network analysis of the peripheral blood from Amyotrophic Lateral Sclerosis patients.

Bmc Genomics

Saris, Christiaan G J CG; Horvath, Steve S; van Vught, Paul W J PW; van Es, Michael A MA; Blauw, Hylke M HM; Fuller, Tova F TF; Langfelder, Peter P; DeYoung, Joseph J; Wokke, John H J JH; Veldink, Jan H JH; van den Berg, Leonard H LH; Ophoff, Roel A RA

Publication Date: 2009-08-27

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PubMed Link: 19712483

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• 1471-2164-10-405.pdf

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The distinct roles of cyclooxygenase-1 and -2 in neuroinflammation: implications for translational research.

Trends In Pharmacological Sciences

Choi, Sang-Ho SH; Aid, Saba S; Bosetti, Francesca F

Publication Date: 2009-04

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PubMed Link: 19269697

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